What is Doose Syndrome?

Myoclonic astatic epilepsy (MAE), also known as Doose syndrome, is an epilepsy syndrome

epilepsy syndrome

Severe syndromes with diffuse brain dysfunction caused, at least partly, by some aspect of epilepsy, are also referred to as epileptic encephalopathies. These are associated with frequent seizures that are resistant to treatment and severe cognitive dysfunction, for instance Lennox-Gastaut syndrome and West syndrome.

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Epilepsy syndromes - Wikipedia

of early childhood, most commonly appearing between ages 1 and 5 and featuring generalized seizures. Children will experience drop attacks and staring seizures, sometimes associated with falls.

What is the cause of Doose syndrome?

Doose syndrome is a rare form of early childhood epilepsy that usually begins between the ages of 1 and 5. The median age at onset is 3 years old. Children are usually developing normally prior to onset. Currently, the cause of this condition is still undetermined though it is believed to be genetic.

Can you outgrow Doose syndrome?

While seizures often respond poorly to medication, about 2 out of 3 children ultimately outgrow their epilepsy and can wean off medication. About one third have persisting seizures. Development typically improves once seizures are controlled, with some children returning to normal function.

Is there a cure for Doose syndrome?

Anti-seizure medications are the most common way to treat Doose syndrome. These medications are in liquid form that your child can drink or a pill that your child can swallow. The Ketogenic diet is a high-fat, low-carb diet for children who don't respond well to medications.

Is Doose syndrome a disability?

Doose syndrome is not a guarantee of long term intellectual disability, but it will take a holistic approach to maximize your child's potential outcome. In 94% of the cases, epilepsy starts within the first five years of life. Often this occurs between 2 and 3 but can range from as early as one month to five years.

Pediatric Epilepsy Syndromes – Mayo Clinic

What do drop seizures look like?

Part or all of the body may become limp. The eyelids may droop, the head may nod or drop forward, and the person may drop things. If standing, the person often falls to the ground. These seizures typically last less than 15 seconds.

What causes non epileptic seizures?

NES is most often caused by mental stress or a physical condition, including: A heart condition that causes fainting. Diabetes or other metabolic disorders. Emotional pain.

What causes childhood absence epilepsy?

Childhood absence epilepsy is a type of epilepsy. The seizures associated with epilepsy occur as a result of uncontrollable bursts of electrical activity in the brain. The underlying cause of the condition is generally genetic, though environmental factors may contribute to its onset in some cases.

What is a head drop seizure?

Atonic seizures, or drop attacks, are brief seizures that cause sudden muscle limpness. You might fall or drop an item. In babies and children, the head might drop. These seizures are rare. They're more common in children than adults, as they typically appear in childhood.

What is the most common epilepsy syndrome?

Benign rolandic epilepsy (BRE), childhood idiopathic occipital epilepsy (CIOE), childhood absence epilepsy (CAE), and juvenile myoclonic epilepsy (JME) are some of the common epilepsy syndromes in the pediatric age group. Among the four, BRE is the most commonly encountered.

Is it OK to sleep after seizure?

After the seizure: they may feel tired and want to sleep. It might be helpful to remind them where they are. stay with them until they recover and can safely return to what they had been doing before.

Do seizures damage the brain?

Most types of seizures do not cause damage to the brain. However, having a prolonged, uncontrolled seizure can cause harm. Because of this, treat any seizure lasting over 5 minutes as a medical emergency.

What is the average lifespan of someone with epilepsy?

On average, people with epilepsy live 10–12 years less than those who do not have the condition. Summary: On average, people with epilepsy live 10-12 years fewer than those who do not have the condition. Excess mortality is particularly pronounced among people with epilepsy and mental disorders.

Can seizures be caused by anxiety?

Seizures can occur due to a variety of triggers, including increased stress and anxiety. However, the Epilepsy Foundation suggests that it's hard to know exactly how often stress triggers seizures.

What is the life expectancy of a child with West syndrome?

West syndrome is generally not life-threatening but it occurs more often in children with life-threatening conditions. Furthermore, the treatments used for West syndrome can (rarely) cause death. As a result, only 5 out of every 100 children diagnosed with West syndrome will not survive beyond the age of five years.

Is Lennox-Gastaut Syndrome fatal?

People with Lennox-Gastaut syndrome have a higher risk of death than their peers of the same age. Although the increased risk is not fully understood, it is partly due to poorly controlled seizures and injuries from falls.

What are the 4 types of seizures?

There are four main types of epilepsy: focal, generalized, combination focal and generalized, and unknown. A doctor generally diagnoses someone with epilepsy if they have had two or more unprovoked seizures. Medication is the most common treatment, and two-thirds of adults with epilepsy live seizure-free because of it.

What are the first signs of a seizure?

What is a stare seizure?

An absence seizure causes you to blank out or stare into space for a few seconds. They can also be called petit mal seizures. Absence seizures are most common in children and typically don't cause any long-term problems. These types of seizures are often set off by a period of hyperventilation.

At what age do absence seizures stop?

In about 7 out of 10 children with absence seizures, the seizures may go away by age 18. If this happens, medicines may not be needed as an adult. Children who start having absence seizures before age 9 are much more likely to outgrow them than children whose absence seizures start after age 10.

Is epilepsy linked to ADHD?

Attention-deficit/hyperactivity disorder (ADHD) occurs more frequently in people with epilepsy than in the general population. Children with ADHD have an increased risk of seizures, with approximately 14% of children with ADHD developing seizures. ADHD is the most common co-occurring disorder in children with epilepsy.

Do children outgrow absence seizures?

About 65% of children with childhood absence epilepsy do outgrow their seizures and are able to stop taking medication. The chance that the seizures will be outgrown is lower in those who have: learning problems.

Can emotional trauma cause seizures?

Yes, trauma can lead to non-epileptic seizures. In this case, the seizure is rooted in a psychological disturbance, rather than chronic issues related to disruptions in the electrical activity of the brain.

Can low blood sugar trigger a seizure?

Not enough glucose can impair the brain's ability to function. Severe or long-lasting hypoglycemia may cause seizures and serious brain injury.

Can I drive with non-epileptic seizures?

The majority of the experts considered that individuals with active PNES should generally not be allowed to drive if any of the following criteria are met: Loss of awareness/responsiveness with their psychogenic seizures.