What are the symptoms of limited scleroderma?

How do I know if I have limited scleroderma?

Limited Scleroderma

The skin hardening and tightening is limited usually just to the fingers and sometimes the hands, forearms or the face. Internal organ damage is less likely in the limited scleroderma type. In general, patients with limited scleroderma have a normal life expectancy.

How is limited scleroderma treated?

How common is limited scleroderma?

Approximately one in 10,000 individuals is affected. It is more common in women and most often develops around age 30 to 50. Systemic scleroderma can affect almost any organ in the body, and there is a large variability of symptoms among affected individuals.

What is the difference between limited scleroderma?

Scleroderma is often categorized as "limited" or "diffuse," which refers only to the degree of skin involvement. Both types can involve any of the other vascular or organ problems. Localized scleroderma, also known as morphea, affects only the skin.

Scleroderma Subtypes (5 Types of Systemic Sclerosis incl. Limited vs Diffuse Scleroderma)

Can limited scleroderma be mild?

There are different types of systemic sclerosis – diffuse and limited. Diffuse systemic sclerosis can affect skin all over the body and is more likely to affect the internal organs. Limited systemic sclerosis is a milder form that only affects the skin on the face, lower arms, hands, lower legs and feet.

Can limited scleroderma go into remission?

Scleroderma varies from person to person

Some people can have mild symptoms and no involvement other than the skin, while others can have serious health issues as a result. For most people, symptoms flare up and then go into remission for a period of time before flaring up again.

Is limited scleroderma hereditary?

Genetics plays a role in the disease, but it is not passed on from parents to children, and it's rare for immediate family members of those with scleroderma to get it. It is common for family members, however, to have other autoimmune diseases such as thyroid disease, rheumatoid arthritis or lupus.

What does a scleroderma flare up feel like?

Common symptoms of scleroderma may include painful joints (arthralgia), morning stiffness, fatigue, and/or weight loss. The intermittent loss (triggered by cold temperatures) of blood supply to the fingers, toes, nose, and/or ears (Raynaud's phenomenon) is an early and frequent complaint of people with scleroderma.

Is limited scleroderma progressive?

Limited scleroderma is a chronic but slowly progressive condition. Importantly, patients usually do not usually expire from the disease.

What is the mildest form of scleroderma?

Localised scleroderma is the mildest form of the condition. It often affects children, but can occur at any age. This type just affects the skin, causing 1 or more hard patches to develop. Internal organs aren't affected.

Is limited systemic sclerosis serious?

Patients with limited systemic sclerosis (CREST syndrome) may have disease that is nonprogressive for long periods; visceral changes (eg, pulmonary hypertension caused by vascular disease of the lung, a peculiar form of biliary cirrhosis) eventually develop, but the course is often remarkably benign.

Is limited scleroderma systemic?

In this type of scleroderma, systemic scleroderma, the internal organs are affected as well as the skin. The heart, oesophagus, blood vessels, kidneys, lungs, blood pressure and digestive system can all be involved.

Is CREST syndrome the same as limited scleroderma?

A less severe form of scleroderma is called limited scleroderma, or CREST syndrome. CREST syndrome is characterized by: Calcinosis: Calcium skin deposits. Raynaud's phenomenon: A condition in which the blood vessels of the fingers and toes spasm when triggered by factors, such as cold, stress or illness.

What should I avoid with scleroderma?

Avoid foods that may aggra- vate symptoms such as citrus fruits, tomato products, greasy fried foods, coffee, garlic, onions, peppermint, gas-producing foods (such as raw peppers, beans, broccoli or raw onions), spicy foods, carbonated beverages and alcohol.

What environmental triggers cause scleroderma?

Environmental factors

Some evidence points to possible environmental triggers of scleroderma. For example, infections by some viruses and long-term exposure to some chemicals, such as pesticides, silica dust, or polyvinyl chloride, are thought to be linked to the disease.

Is scleroderma worse than lupus?

Patients with systemic sclerosis (SSc) have worse health-related quality of life than patients with other systemic rheumatic diseases such as rheumatoid arthritis (RA) and systemic lupus erythematosus (SLE), a Korean study found.

Where does scleroderma usually start?

Another early sign of systemic scleroderma is puffy or swollen hands before thickening and hardening of the skin due to fibrosis. Skin thickening usually occurs first in the fingers (called sclerodactyly) and may also involve the hands and face.

What is the newest treatment for scleroderma?

Two drugs are currently FDA approved to treat lung scarring, or pulmonary fibrosis, that occurs as a result of scleroderma: nintedanib and tocilizumab.

Does scleroderma cause weight gain?

Acute localized scleroderma (morphea) can present as severe generalized oedema with rapid weight gain and oliguria.

Does heat make scleroderma worse?

The sun, heat and even air-conditioning can intensify symptoms and cause problems that linger for months, if not years. For doctors who manage those diseases, primarily lupus, scleroderma and Raynaud's phenomenon, the challenges of educating their patients about sun avoidance become greater, too.

Does scleroderma affect the feet?

Foot pain and lesion are common in Scleroderma patients, the diffuse subtype of the diseases, foot's Raynaud's, calcinosis, and telangiectasia were independently associated factors with foot lesion.

What is limited systemic sclerosis?

Limited cutaneous systemic sclerosis is a subtype of systemic sclerosis characterized by the association of Raynaud's phenomenon and skin fibrosis on the hands, face, feet and forearms.

What is the scleroderma skin pinch test?

“In using a skin scoring system, the physician pinches various parts of the patient's body to test for thickness. The less skin that can be pinched equals a higher score in diagnosing scleroderma,” says Feghali-Bostwick.